Primary Undifferentiated Small Round Cell Sarcoma of Sellar Region: A Case Report and Literature Review
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摘要: 目的：探讨鞍区原发性小圆细胞性未分化肉瘤的临床表现、病理特征及影像特点，以提高对该病的影像诊断及鉴别诊断能力。方法：回顾性分析1例经手术病理证实为鞍区原发性小圆细胞性未分化肉瘤的临床病理特征、CT及MR表现，并复习文献。结果：CT平扫示鞍区偏右侧呈稍低密度影，增强欠均匀强化，并累及邻近颅骨；MRI示T1WI呈低信号，T2WI、液体衰减反转恢复（FLAIR）呈略高信号，扩散加权成像（DWI）序列上呈高信号，信号欠均匀；增强病灶较明显强化，边缘较光整，邻近蝶鞍后床突可见骨质破坏。结论：鞍区原发性小圆细胞未分化肉瘤罕见，其临床和影像表现无明显特异性，确诊仍需依靠病理组织学检查。
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关键词:
- CT诊断 /
- 鞍区 /
- 未分化/未分类软组织肉瘤
Abstract: Objective: This study aimed to investigate the clinical, pathological, and imaging features of primary undifferentiated small round cell sarcoma of the sellar region to improve the ability of imaging and differential diagnosis. Methods: The clinicopathological features and computed tomography (CT) and magnetic resonance imaging (MRI) manifestations of a case with primary undifferentiated small round cell sarcoma of the sellar region confirmed by surgery and pathology were retrospectively analyzed, and the literature was reviewed and summarized. Results: CT showed a node in the right sellar region, reinforcement under-uniform reinforcement and affects adjacent skull; MRI showed homogeneous hypointensity on the T1-weighted image, hyperintense on the T2-weighted image, fluid-attenuated inversion recovery, and diffusion-weighted imaging; and significantly reinforcement with smooth margin on reinforcement scanning. Bone destruction was seen near the posterior clinoid process of the sella turcica. Conclusion: Primary undifferentiated small round cell sarcoma of the sellar region is rare, and its clinical and imaging findings are not significantly specific. Therefore, the diagnosis requires histopathological examination.-
Key words:
- CT /
- sellar region /
- undifferentiated/unclassified soft tissue sarcoma
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