ISSN 1004-4140
CN 11-3017/P
洪天予, 张祺丰, 李笛, 等. CT在评估婴儿型和成人型弯刀综合征的临床应用价值[J]. CT理论与应用研究(中英文), 2024, 33(5): 633-639. DOI: 10.15953/j.ctta.2023.221.
引用本文: 洪天予, 张祺丰, 李笛, 等. CT在评估婴儿型和成人型弯刀综合征的临床应用价值[J]. CT理论与应用研究(中英文), 2024, 33(5): 633-639. DOI: 10.15953/j.ctta.2023.221.
HONG T Y, ZHANG Q F, LI D, et al. Clinical Application Value of CT in Evaluating Infantile and Adult Scimitar Syndrome[J]. CT Theory and Applications, 2024, 33(5): 633-639. DOI: 10.15953/j.ctta.2023.221. (in Chinese).
Citation: HONG T Y, ZHANG Q F, LI D, et al. Clinical Application Value of CT in Evaluating Infantile and Adult Scimitar Syndrome[J]. CT Theory and Applications, 2024, 33(5): 633-639. DOI: 10.15953/j.ctta.2023.221. (in Chinese).

CT在评估婴儿型和成人型弯刀综合征的临床应用价值

Clinical Application Value of CT in Evaluating Infantile and Adult Scimitar Syndrome

  • 摘要: 目的:本文旨在分析弯刀综合征的CT影像学特征及临床意义,以提高对该病的认识。方法:搜集2019年1月至2024年1月确诊弯刀综合征的患者28例,回顾性分析其临床及影像学资料。结果:28例中男10例,女18例;婴儿型15例,成人型13例。婴儿型平均年龄约(6.78±3.50)月,10例为完全右肺静脉异位引流至下腔静脉,其中3例异位引流处狭窄梗阻,2例合并房间隔缺损及肺动脉高压,该5例行手术治疗;5例为部分右侧肺静脉异位引流至下腔静脉,均合并其他畸形及肺部感染行影像检查时发现。成人型平均年龄约(5.53±2.72)岁,7例为完全右肺静脉异位引流至下腔静脉,其中1例行手术治疗;6例为右下肺静脉异位引流至下腔静脉,其中2例因明确诊断多年行择期手术,2例因叶外型隔离肺行介入治疗体动脉分支供血。结论:婴儿型和成人型弯刀综合征患儿的临床表现有很大差异,利用CT检查的多种成像模式,结合强大重建后处理功能对弯刀综合征患儿进行全面评估,可为临床上治疗方法的选择、手术方案的制定提供依据。

     

    Abstract: Objective: This article aimed to analyze the computed tomography (CT) imaging manifestations and clinical significance of scimitar syndrome to improve our understanding of the disease. Method: A total of 28 patients diagnosed with scimitar syndrome were enrolled in our hospital from January 2019 to January 2024, and their clinical and imaging data were retrospectively analyzed. Results: Among the 28 cases, there were 10 males and 18 females, with 15 and 13 cases of the infantile and adult types, respectively. The average age of patients with the infant type were (6.78±3.50) months, with 10 cases having total anomalous right pulmonary venous drainage. Among them, three cases had stenosis and obstruction at the site of ectopic drainage and two cases had concomitant atrial septal defect and pulmonary arterial hypertension; these five cases underwent surgical treatment. Five cases of partial anomalous right pulmonary venous drainage to the inferior vena cava were found during imaging examination owing to the presence of other deformities and pulmonary infections. The average age of patients with the adult type was (5.53±2.72) years old. Seven cases had total anomalous right pulmonary venous drainage to the inferior vena cava, with one case undergoing surgical treatment. Six cases had ectopic drainage from the right lower pulmonary vein to the inferior vena cava: two underwent elective surgery owing to a clear diagnosis for many years, and two underwent interventional treatment for systemic arterial blood supply owing to extralobar sequestration. Conclusion: There were significant differences in clinical manifestation between patients with infantile and adult types of scimitar syndrome. Using multiple imaging modes of CT examination combined with powerful reconstruction post-processing functions, children with scimitar syndrome can be evaluated comprehensively, providing a basis for the selection of clinical treatment methods and surgical plans.

     

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