CT诊断左肺静脉缺如并左肺动脉发育不良案例分析

刘书燕; 鄂林宁

doi:10.15953/j.ctta.2024.108

CT诊断左肺静脉缺如并左肺动脉发育不良案例分析

刘书燕^{1, 2,},
鄂林宁^3, ,

1.
山西医科大学医学影像学院，太原 030001
2.
山西白求恩医院（山西医学科学院）放射科，太原 030032
3.
深圳市龙华区人民医院医学影像科，广东深圳 518109

基金项目: 山西省医学重点科研项目（2022XM42）。

详细信息

作者简介:
刘书燕: 女，山西医科大学放射影像学专业在读硕士研究生，主要从事胸部影像学研究，E-mail：1741042992@qq.com

通讯作者:
鄂林宁: 男，医学博士，博士生导师，深圳市龙华区人民医院影像科副主任、主任医师，主要研究领域为呼吸系统疾病影像诊断，E-mail：elinning@163.com。

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出版历程
- 收稿日期: 2024-06-22
- 修回日期: 2024-08-14
- 录用日期: 2024-08-14
- 网络出版日期: 2024-08-22

A case Study of Absence of the Left Pulmonary Vein with Left Pulmonary Artery Hypoplasia Diagnosed by CT

LIU Shuyan^{1, 2,},
E Linning^3, ,

1.
College of Medical Imaging, Shanxi Medical University, Taiyuan 030001, China
2.
Department of Radiology, Shanxi Bethune Hospital (Shanxi Academy of Medical Sciences), Taiyuan 030032, China
3.
Department of Radiology, People's Hospital of Longhua District, Shenzhen 518109, China

摘要

摘要:
单侧肺静脉缺如（UPVA）是一种罕见的先天性畸形，CT血管成像能够清晰地显示肺动脉和肺静脉的解剖形态及相关病变。本文报告1例无症状的28岁成年女性患者，肺部CT平扫表现为单侧肺间质性改变，CT血管成像诊断为UAPV，其各项实验室检查均未见异常。结合相关文献对UAPV的影像学表现进行总结分析，以提高对该疾病的认识和诊断水平。
- 肺静脉 /
- 体层摄影术 /
- X线计算机 /
- 先天畸形
Abstract:
Unilateral absence of the pulmonary vein (UAPV) is a rare congenital anomaly, and computed tomography (CT) angiography can clearly show the anatomical morphology of the pulmonary artery, pulmonary vein, and related lesions. Here, we report the case of an asymptomatic 28-year-old female patient with unilateral interstitial changes in the lungs on plain CT scanning due to UAPV, diagnosed on CT angiography, with no abnormalities in her laboratory tests. This report summarizes and analyzes the imaging manifestations of UAPV in conjunction with related literature to improve our understanding and the diagnosis of this rare disease.
- pulmonary veins /
- tomography /
- X-ray computer /
- congenital anomalies

HTML全文

图 1 患者，女性，29岁，左肺静脉缺如并左肺动脉发育不良

注：（a）胸部CT平扫可见左肺体积减小，箭头所指为左侧肺门区域，显示左肺体积缩小，肺野内可见杂乱的线状影及网格状影，与右侧肺门对比，左肺门区血管稀少、纤细且走行僵直；（b）（c）箭头所指分别为左、右肺动脉主干，显示左肺动脉与右肺动脉之间存在显著的尺寸差异，左肺动脉主干及其分支明显纤细，右肺动脉及其分支扩张增粗，且左肺门处可见软组织影包绕；（d）为轴位CTA图像，箭头所指为左心房左侧缘，显示左心房边缘光滑，未见左肺静脉显影，右肺静脉及其分支扩张增粗；（e）为肺动脉成像，箭头所指为左肺动脉主干，显示左肺动脉主干及其分支明显纤细；（f）为肺静脉成像，箭头所指为左心房左侧缘，显示左心房左侧缘边缘光滑，未见左肺静脉显影。

Figure 1. Female patient aged 29 years with absence of the left pulmonary vein and left pulmonary artery hypoplasia

下载: 全尺寸图片幻灯片

图 2 患者随访图像

注：（a）胸部CT平扫可见左肺体积减小，箭头所指为左侧肺门区域，显示左肺体积缩小，肺野内可见杂乱的线状影及网格状影，与右侧肺门对比，左肺门区血管稀少、纤细且走行僵直；（b）（c）箭头所指分别为左、右肺动脉主干，显示左肺动脉与右肺动脉之间存在显著的尺寸差异，左肺动脉主干及其分支明显纤细，右肺动脉及其分支扩张增粗；（d）为轴位CTA图像，箭头所指为左心房左侧缘，显示左心房边缘光滑，未见左肺静脉显影，右肺静脉及其分支扩张增粗；均较2020年10月图像未见明显变化。

Figure 2. Follow-up images of the patient

下载: 全尺寸图片幻灯片

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